ASS1 Antibody 1 Publications

Mouse Monoclonal| Catalog number: 66036-1-Ig |CloneNo.: 1D1A11

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Freight/Packing

Con: 150 μg/150 μl

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Species specificity:
human, pig

Positive WB detected in:
pig liver tissue, HeLa cells, human liver tissue, L02 cells

Positive IHC detected in:
human liver tissue, human liver tissue, human liver cancer tissue, human testis tissue

Positive IF detected in:
MCF-7 cells

Recommended dilution:
WB : 1:1000-1:8000
IHC : 1:250-1:1000
IF : 1:20-1:200

Product Information


Source:
Mouse

Purification method:
Protein G purification

Isotype:
IgG1

Storage:
PBS with 0.02% sodium azide and 50% glycerol pH 7.3. Store at -20oC. Aliquoting is unnecessary for -20oC storage.

Immunogen Information


Full name:
argininosuccinate synthetase 1

Calculated molecular weight:
412aa,47 kDa

Observed molecular weight:
40-45 kDa

GenBank accession number:

Gene ID (NCBI):

Gene symbol
ASS1

Synonyms
Argininosuccinate synthase, argininosuccinate synthetase 1, ASS, ASS1, Citrulline aspartate ligase, CTLN1
Background

ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype(PMID:19006241).


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