FBN1-Specific Antibody 0 Publications

Rabbit Polyclonal| Catalog number: 20251-1-AP

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Freight/Packing

Con: 36 μg/150 μl

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Species specificity:
human, mouse, rat

Recommended dilution:

Product Information


Source:
Rabbit

Purification method:
Antigen affinity purification

Isotype:
IgG

Storage:
PBS with 0.1% sodium azide and 50% glycerol pH 7.3. Store at -20oC. Aliquoting is unnecessary for -20oC storage.

Immunogen Information


Immunogen:
Peptide

Full name:
fibrillin 1

Calculated molecular weight:
312 kDa

Observed molecular weight:

GenBank accession number:

Gene ID (NCBI):

Gene symbol
FBN1

Synonyms
FBN, FBN1, fibrillin 1, MASS, MFS1, OCTD, SGS, WMS
Background

FBN1, also named as FBN, belongs to the fibrillin family. Fibrillins are structural components of 10-12 nm extracellular calcium-binding microfibrils, which occur either in association with elastin or in elastin-free bundles. Fibrillin-1-containing microfibrils provide long-term force bearing structural support. Defects in FBN1 are a cause of Marfan syndrome (MFS), isolated ectopia lentis (EL), Weill-Marchesani syndrome autosomal dominant (ADWMS), Shprintzen-Goldberg craniosynostosis syndrome (SGS) or MASS syndrome. This antibody is specific to FBN1.


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